MELAS Syndrome with Cardiac Involvement: A Multimodality Imaging Approach

نویسندگان

  • Sara Seitun
  • Laura Massobrio
  • Anna Rubegni
  • Claudia Nesti
  • Margherita Castiglione Morelli
  • Sara Boccalini
  • Athena Galletto Pregliasco
  • Irilda Budaj
  • Luca Deferrari
  • Gian Marco Rosa
  • Fabrizio Montecucco
  • Alberto Valbusa
چکیده

A 49-year-old man presented with chest pain, dyspnea, and lactic acidosis. Left ventricular hypertrophy and myocardial fibrosis were detected. The sequencing of mitochondrial genome (mtDNA) revealed the presence of A to G mtDNA point mutation at position 3243 (m.3243A>G) in tRNALeu(UUR) gene. Diagnosis of cardiac involvement in a patient with Mitochondrial Encephalomyopathy, Lactic Acidosis, and Stroke-like episodes syndrome (MELAS) was made. Due to increased risk of sudden cardiac death, cardioverter defibrillator was implanted.

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عنوان ژورنال:

دوره 2016  شماره 

صفحات  -

تاریخ انتشار 2016